Pharmacological Improvement of Cystic Fibrosis Transmembrane Conductance Regulator Function Rescues Airway Epithelial Homeostasis and Host Defense in Children with Cystic Fibrosis
Most Cited Paper
in Pediatric health and respiratory diseases
18 Months Post-Publication
Class of 2026
“Pharmacological Improvement of Cystic Fibrosis Transmembrane Conductance Regulator Function Rescues Airway Epithelial Homeostasis and Host Defense in Children with Cystic Fibrosis”
A research intelligence initiative by Pepkio
pri.pepkio.com/top-papers/pediatric-health-and-respiratory-diseases/2026/
Topics
CFTR · CFTR · Elexacaftor/tezacaftor/ivacaftor · Elexacaftor/tezacaftor/ivacaftor · F508del mutation · nasal epithelial cells · single-cell RNA sequencing · ionocytes · Airway basal cells · club cells · goblet cells · IFN signaling · major histocompatibility complex class I · major histocompatibility complex class II · neutrophils · macrophages · Airway mucosal homeostasis · innate mucosal immunity · CFTR-positive cells · immune cell inflammatory responses
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Pepkio Research Index (PRI). Topics and Trends in Most Cited Pediatric health and respiratory diseases Papers, Class of 2026. https://pri.pepkio.com/top-papers/pediatric-health-and-respiratory-diseases/2026. Accessed 2026-07-13. Zheng Su, Tinsley Li, Thematic Shifts in Early-High-Impact Cancer Genomics and Diagnostics Research: A Bibliometric and Semantic Analysis. bioRxiv 2026.07.04.736459; doi: https://doi.org/10.64898/2026.07.04.736459