Multisystemic Effects of Elexacaftor–Tezacaftor–Ivacaftor in Adults with Cystic Fibrosis and Advanced Lung Disease

Topics

Elexacaftor/Tezacaftor/Ivacaftor · cystic fibrosis · advanced lung disease · ppFEV1 ≤40 · CFTR modulator · cystic fibrosis liver disease · cystic fibrosis-related diabetes · FEV1 · body mass index · vitamin A · vitamin E · 25-hydroxy vitamin D3 · oxygen therapy · noninvasive ventilation · nutritional support · insulin discontinuation · Lung transplantation · inhaled antibiotics

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Pepkio Research Index (PRI). Topics and Trends in Most Cited Pediatric health and respiratory diseases Papers, Class of 2026. https://pri.pepkio.com/top-papers/pediatric-health-and-respiratory-diseases/2026. Accessed 2026-08-20.

Methodology
Zheng Su, Tinsley Li, Thematic Shifts in Early-High-Impact Cancer Genomics and Diagnostics Research: A Bibliometric and Semantic Analysis. bioRxiv 2026.07.04.736459; doi: https://doi.org/10.64898/2026.07.04.736459